Pathways of ammonia detoxification to GLN in muscles affiliated with enhanced use from the BCAA and ?-KG (cataplerosis) and prompt results of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Constructive influence of BCAA on ammonia detoxification to GLN could be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenyl